Kliniken &… SFB / DZG SFB 938 Publikationen

Projekt I - Gröne/Porubsky

Renal lipidosis in patients enrolled in a methadone substitution program.
Porubsky S, Kuppe C, Maier T, Birk HW, Wörnle M, Moeller MJ, Floege J, Gröne HJ.
Arch Pathol Lab Med. 2014 May;138(5):689-93.

Depletion of globosides and isoglobosides fully reverts the morphologic phenotype of Fabry disease.
Porubsky S; Jennemann R; Lehmann L; Gröne HJ.
Cell and Tissue Research, in press

Sulfatides are required for renal adaptation to chronic metabolic acidosis (PDF)
Paula Stettnera, Soline Bourgeoisb, Christian Marsching, Milena Traykova-Braucha, Stefan Porubskya, Viola Nordströma, Carsten Hopfd, Robert Köstersf, Roger Sandhoff, Herbert Wiegandta, Carsten A. Wagnerb, Hermann-Josef Grönea, Richard Jennemanna

Neuronal Expression of Glucosylceramide Synthase in Central Nervous System Regulates Body Weight and Energy Homeostasis (PDF)
Viola Nordström, Monja Willershäuser, Silke Herzer, Jan Rozman, Oliver von Bohlen und Halbach, Sascha Meldner, Ulrike Rothermel, Sylvia Kaden, Fabian C. Roth, Clemens Waldeck, Norbert Gretz, Martin Hrabe de Angelis, Andreas Draguhn, Martin Klingenspor, Hermann-Josef Gröne, Richard Jennemann

Lipid Droplet Accumulation Is Associated with an Increase in Hyperglycemia-Induced Renal Damage Prevention by Liver X Receptors (PDF)
Eva Kiss, Bettina Kränzlin, Katja Wagenblab, Mahnaz Bonrouhi, Joachim Thiery, Elisabeth Gröne, Viola Nordström, Daniel Teupser, Norbert Gretz, Ernst Malle, Hermann-Josef Gröne

Globosides but Not Isoglobosides Can Impact the Development of Invariant NKT Cells and Their Interaction with Dendritic Cells (PDF)
Stefan Porubsky, Anneliese O. Speak, Mariolina Salio, Richard Jennemann, Mahnaz Bonrouhi, Rashad Zafarulla,Yogesh Singh, Julian Dyson, Bruno Luckow, Agnes Lehuen, Ernst Malle, Johannes Müthing, Frances M. Platt, Vincenzo Cerundolo and Hermann-Josef Gröne

A new, robust, and nonradioactive approach for exploring N-myristoylation (PDF)
Francesca Rampoldi , Roger Sandhoff , Robert W. Owen , Hermann-Josef Gröne , Stefan Porubsky